Purpose Fibroepithelial polyps (FEP) are rare, benign lesions of mesodermal origin. Ureteric FEP are extremely rare, with less than 200 cases reported in children over the past 20 years. The purpose of this study is to present: 1. A retrospective review of ureteric FEP at two centres 2. A systematic literature review of ureteric FEP in children Methodology Retrospective review of seven children with upper tract FEP managed at Townsville University Hospital and Queensland Children’s Hospital. Systematic review of all seven original articles reporting three or more cases of upper tract, FEP in children from January 2003 to November 2023. Results Seven children, with a mean age of 10.3 years (range 5.5-14) were managed with ureteric FEP. The majority were male (n=6/7) and left sided (n=5/6). The most common presenting features were pain and haematuria. Three children had a prolonged history of symptoms (range 2-10years). Diagnosis was challenging with numerous imaging studies utilised including: ultrasound, cross sectional imaging, functional studies and operative retrograde pyelogram/ureteroscopy. The majority were managed with laparoscopic pyeloplasty (n=6/7) with one case converted to open. The systematic literature review revealed a total of 134 children. 93% were male and 84% of polyps were left sided. Numerous operative approaches were reported. There was n=1/134 case of urothelial papilloma on histology with the remainder being benign FEP. Conclusion Ureteric FEP are a rare pathology typically seen in males and on the left side. Diagnosis can be challenging. Various management options have been reported depending on surgeon experience, size and location of the polyp.